ABSTRACT
Infantile myofibromatosis [IM] is an extremely rare cause of skull lesion in the new-born and paediatric population. The prognosis is related to the number of lesions and the presence or absence of visceral involvement. The authors report a case of IM, in a 5-year-old boy with an osteolytic lesion in the right orbital roof, which displaced the globe downwards. A subfrontal approach was made with total resection. The globe had regained a normal position and further evaluation revealed no other lesions. The patient's age at presentation, physical findings, radiographic appearance and the histopathological examination of the lesion are needed to generate a-differential diagnosis and to formulate a treatment plan
Subject(s)
Humans , Male , Orbital Neoplasms , Pediatrics , Tomography, X-Ray ComputedABSTRACT
Spinal epidural haematoma can be secondary to congential acquired coagulation disorder or rupture of a vascular malformation. However, sometimes none of these aetilogies are present, as in the case of our patient. The authors report a case of lumbar spontaneous epidural haematoma causing complications of a malignant systemic arterial hypertension in a 48-year-old patient, who had not presented signs of arterial hypertension previously. In this study, we discuss the clinical aspects, pathogenesis and exploration methods of this rare disease. Its characteristics are that it appears suddenly and constitutes a therapeutic emergency